Periodic family paralysis

Periodic family paralysisPERIODIC FAMILY PARALYSIS (paroxysmal family diplegia) is a hereditary disease characterized by sudden acute transient attacks of flaccid paralysis of the limbs. Etiology, pathogenesis. The cause of the disease is unknown. The basis of pathogenesis lies transient ischemic potassium levels in the blood. The symptoms for. The first attacks of muscle weakness appear in childhood or young age. In most cases, the attack begins early in the morning. Paralysis of the muscles usually reach a peak within one hour, symmetrically straddle legs (mainly the proximal departments); sometimes there is only weakness of the lower extremities. Bulbar, eye and respiratory muscles in the process is usually not involved. The flaccid paralysis, hypotonia and areflexia. Sensitivity is maintained. Consciousness is not disturbed. Typically a significant reduction in the level of potassium in the blood. The paralysis can last from several minutes to several hours. In the interictal period with this paralysis healthy. Thus, the disease can be considered benign. Only in very rare cases, the involvement of respiratory muscles can lead to death. Differential diagnosis with other forms of developing acute paralysis (spinal stroke, polyneuropathy) is based on the frequency of attacks of paroxysmal diplegia and strict selectivity flaccid paralysis (without other symptoms of the nervous system.) Finally confirms the diagnosis found at the height of the attack of sharp hypokalemia. In some cases periodic paralysis is observed in the normal or even increased amounts of potassium in the urine (renal failure in particular). Treatment. During an attack inside designate 5-10 g of potassium chloride. When respiratory failure-in/introduction of potassium. With the preventive purpose shows the potassium chloride several times a day inside, as well as a systematic method diakarba..



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